
Extra mammary Paget′s disease of the vulva
Author(s) -
Debabrata Barmon,
Amal Chandra Kataki,
Lima Imchen,
Jagannath Dev Sharma
Publication year - 2012
Publication title -
journal of mid-life health
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.423
H-Index - 11
eISSN - 0976-7819
pISSN - 0976-7800
DOI - 10.4103/0976-7800.104474
Subject(s) - vulva , medicine , wide local excision , disease , paget disease , postmenopausal women , surgery , dermatology
Extra mammary Paget's disease (EMPD) is a rare condition, which affects postmenopausal women. Wide local excision may not be appropriate in elderly patients with extensive disease. It is an uncommon malignant neoplasia with a high local recurrence rate. The standard treatment is local excision of the affected area with adequate margins; however, 40~45% of cases recur after surgery within 4 years. Although surgery is currently considered the preferred primary treatment for EMPD, it has a high relapse rate due to the multifocal nature of the disease. Hence, RT in selected cases of EMPD of vulva may be beneficial.