Open AccessMetastatic Intracranial Adenoid Cystic Carcinoma with Unknown Primary: Case Report and Review of Literature
Author(s) -
Jitender Chaturvedi,
Subas Kanti Konar,
Dilip Jethwani,
Dwarakanath Srinivas,
Anita Mahadevan
Publication year - 2017
Publication title -
journal of neurosciences in rural practice
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.331
H-Index - 22
eISSN - 0976-3147
pISSN - 0976-3155
DOI - 10.4103/0976-3147.203810
Subject(s) - medicine , adenoid cystic carcinoma , primary (astronomy) , carcinoma , radiology , dermatology , pathology , physics , astronomy
Adenoid cystic carcinoma (ACC) is an epithelial malignancy comprising approximately 8-10% of all salivary gland tumors. Intracranial ACC without a known primary is an extremely rare pathobiological event. Only 13 cases have been reported in available literature. We report a case of a rare intracranial ACC in a 35-year-old gentleman presenting with features of raised intracranial pressure. Patient had a lesion in the right parieto-occipital lobe and underwent gross total decompression. There was no evidence of any primary after a thorough systemic evaluation. In the postoperative period, he showed a good clinical improvement and was recurrence free at follow-up of 18 months. We also discuss and review the existing relevant literature.