Open AccessSurgical management of a large cleft palate in a Pierre Robin sequence: A case report and review of literature
Author(s) -
S Andrews,
Mathew Sam,
Krishnan Ravindran,
Maya Ramesh,
Shiji M Kunjappan
Publication year - 2015
Publication title -
journal of pharmacy and bioallied sciences
Language(s) - English
Resource type - Journals
eISSN - 0976-4879
pISSN - 0975-7406
DOI - 10.4103/0975-7406.163498
Subject(s) - palatoplasty , pierre robin syndrome , medicine , epiglottis , neonatology , general surgery , pediatrics , surgery , pregnancy , larynx , biology , genetics
Pierre Robin syndrome or Pierre Robin sequence (PRS) is a congenital etiologically heterogeneous condition presenting with various malformations. Here we are reporting the surgical management of an 18-month-old female baby who was referred from Department of Pediatrics with a complaint of a large cleft palate. She was taken up for palatoplasty with consent for elective tracheostomy. After genetic evaluation, the authors conclude that the presented case was a PRS in isolation with mild cardiac anomalies and an inferiorly placed hypoplastic epiglottis. Patient should be followed up and growth modifications of the jaws should be done.