Open AccessBlocked mesocaval shunt with protein C deficiency in a child with extrahepatic portal hypertension
Author(s) -
Nikhil Rao,
Ira Shah,
Sushmita Bhatnagar
Publication year - 2016
Publication title -
medical journal of dr. d y patil university/medical journal of dr. d.y. patil university
Language(s) - English
Resource type - Journals
eISSN - 2278-7119
pISSN - 0975-2870
DOI - 10.4103/0975-2870.167960
Subject(s) - medicine , portal hypertension , shunt (medical) , protein c deficiency , esophageal varices , portal vein thrombosis , protein s deficiency , cardiology , gastroenterology , etiology , thrombosis , venous thrombosis , cirrhosis
Portal vein thrombosis (PVT) is an important cause of extrahepatic portal hypertension in children. A majority of children with PVT of unknown etiology have functional protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We present an 8-year-old boy with portal hypertension with protein C deficiency, who underwent mesocaval shunt surgery due to recurrent episodes of bleeding esophageal varices and subsequently developed a block in the mesocaval shunt due to a thrombotic tendency