Lamellar icthyosis with bilateral cicatricial ectropion: Case report with review of the literature

Lamellar ichthyosis (LI), is a rare genodermatoses, that appears at birth and continues throughout a person's life with an autosomal recessive mode of inheritance. At birth, most affected infants present as collodion babies, and after shedding the membrane, develop scaling over the body in the localized or generalized pattern. Here, we describe this rare condition of lamellar icthyosis with bilateral cicatricial ectropion in a 21-month-old male child. Treatment with topical emollients for skin and eye drops containing antibiotic to prevent secondary infection with eye lubricants were started. We are reporting this case as dermatological and ocular complications had developed in the baby at such a tender age which could have been minimized if treatment were sought earlier by the parents