Open AccessDyke-Davidoff-Masson syndrome: A case report
Author(s) -
Biswajyoti Rath,
Maheswar Samant,
Kali Prasanna Swain,
Ayaz Khurram Mallick
Publication year - 2014
Publication title -
medical journal of dr. d y patil university/medical journal of dr. d.y. patil university
Language(s) - English
Resource type - Journals
eISSN - 2278-7119
pISSN - 0975-2870
DOI - 10.4103/0975-2870.140494
Subject(s) - hemiparesis , facial symmetry , atrophy , psychology , cerebral palsy , neuroimaging , cerebral atrophy , medicine , skull , convulsion , epilepsy , anatomy , neuroscience , physical medicine and rehabilitation , surgery , pathology , lesion
Dyke-Davidoff-Masson Syndrome (DDMS), also called as cerebral hemiatrophy, is a rare clinical condition characterized by seizures, facial asymmetry, contralateral spastic hemiplegia or hemiparesis, with learning difficulties. It is commonly diagnosed in presence of associated radiologic findings, which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. We present a 21-year female with increased frequency of convulsion and abnormal behavior for the last 2 months. She had a known seizure disorder for 15 years and had mental subnormality. On physical examination, she was disoriented with mild right hemiparesis. On CT scan the brain showed unilateral left cerebral atrophy