Open AccessPoland syndrome with absent ribs
Author(s) -
Rupam Kumar Ta,
Sushmita Kaushik,
Abhijit Saha,
Subrata Ghosh,
Mrinmoy Mitra
Publication year - 2014
Publication title -
medical journal of dr. d y patil university/medical journal of dr. d.y. patil university
Language(s) - English
Resource type - Journals
eISSN - 2278-7119
pISSN - 0975-2870
DOI - 10.4103/0975-2870.122795
Subject(s) - poland syndrome , syndactyly , rib cage , dextrocardia , aplasia , medicine , anatomy , agenesis , pectoralis major muscle , hypoplasia , weakness , surgery
Poland syndrome is a rare congenital disorder characterized by ipsilateral absence of pectoralis major muscle. This syndrome is associated with various anomalies such as ipsilateral syndactyly, brachidactyly, dextrocardia, herniation of lung, underdevelopment of upper ribs, aplasia or hypoplasia of breast, etc. Only few cases had been reported with absent ribs in Poland syndrome. We report a rare case of Poland syndrome presented to us with mal-development of his right hemithorax and weakness of right hand