Open AccessOrbital Rosai-Dorfman Disease in a five year-old boy
Author(s) -
Ashref Al-Moosa,
Raed Behbehani,
A. Hussain,
Aiman Ali
Publication year - 2011
Publication title -
middle east african journal of ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.357
H-Index - 25
eISSN - 0975-1599
pISSN - 0974-9233
DOI - 10.4103/0974-9233.90138
Subject(s) - rosai–dorfman disease , medicine , histiocyte , cervical lymphadenopathy , biopsy , disease , dermatology , histiocytosis , radiology , pathology
Rosai-Dorfman disease (RDD) is characterized by histiocytic proliferation and massive cervical lymphadenopathy, although some patients have extra-nodal involvement. We report a case of extranodal RDD in a five-year-old child, initially misdiagnosed as orbital inflammatory disease and treated with oral steroids. A subsequent orbital biopsy three years later confirmed the diagnosis of Rosai Dorfman disease.