Keratosis follicularis spinulosa decalvans: A rare cause of scarring alopecia in two young Indian girls
Author(s) -
UmaG Maheswari,
V Chaitra,
SubbiahS Mohan
Publication year - 2013
Publication title -
international journal of trichology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.494
H-Index - 22
eISSN - 0974-9241
pISSN - 0974-7753
DOI - 10.4103/0974-7753.114713
Subject(s) - dermatology , hyperkeratosis , scarring alopecia , medicine , keratosis , dyskeratosis , scalp
Keratosis follicularis spinulosa decalvans (KFSD) is an X-linked xenodermatosis characterized by scarring alopecia and follicular hyperkeratosis. This condition mainly affects males with females being carriers and will have milder symptoms. We present two sisters with severe form of KFSD, progressing to scarring alopecia.
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