Open AccessA rare presentation of pigmented paravenous retinochoroidal atrophy
Author(s) -
Arshee S Ahmed,
Pukhraj Rishi
Publication year - 2015
Publication title -
oman journal of ophthalmology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.306
H-Index - 16
eISSN - 0974-7842
pISSN - 0974-620X
DOI - 10.4103/0974-620x.149867
Subject(s) - medicine , fundus (uterus) , atrophy , ophthalmology , presentation (obstetrics) , retinal , retinal pigment epithelium , rare disease , pathology , disease , surgery
A 21-year-old female patient presented with gradual progressive loss of vision in both eyes of 12 years duration. Funduscopic examination revealed bone-spicule pigmentation and choroidal and retinal pigment epithelium atrophy along the vascular arcades, with macular involvement in both eyes. The patient was diagnosed with pigmented paravenous retinochoroidal atrophy which is rare disease, uncommon in females, more commonly affecting the paravascular fundus. Very few cases of macular involvement have been reported.