Open AccessPulmonary function testing in infants with tetralogy of Fallot and absent pulmonary valve syndrome
Author(s) -
Adler Salazar,
Christopher Newth,
Robinder G. Khemani,
Jürg Hammer,
Patrick Ross
Publication year - 2015
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.154152
Subject(s) - medicine , interquartile range , tetralogy of fallot , pulmonary function testing , cardiology , airway resistance , pulmonary compliance , tidal volume , vital capacity , pulmonary valve , anesthesia , respiratory system , heart disease , lung , diffusing capacity , lung function
Absent pulmonary valve syndrome (APVS) is found in 3-6% of patients with Tetralogy of Fallot (TOF). Along with findings of TOF, absence of pulmonary valve tissue results in aneurysmal dilatation of the main and branch pulmonary arteries compressing the trachea, main-stem, and intrapulmonary bronchi leading to obstructive airways disease. Our objective was to review pulmonary function tests (PFT) in TOF-APVS patients.