Open AccessAbernethy syndrome, a rare cause of hypoxemia: A case report
Author(s) -
Manoj Kumar Sahu,
Akshay Kumar Bisoi,
Naveen Chandrasekaran Chander,
Sandeep Agarwala,
Sandeep Chauhan
Publication year - 2015
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.149526
Subject(s) - medicine , hypoxemia , hepatopulmonary syndrome , portosystemic shunt , etiology , shunt (medical) , shunting , cardiology , portal hypertension , cirrhosis
Abernethy syndrome (congenital extrahepatic portosystemic shunt (CEPS II)) as an etiology of hepatopulmonary syndrome (HPS) is uncommon. The severe hypoxemia and its consequences become incapacitating for the patient. Early shunt closure resolves hypoxemia and clinical symptomatology and prevents irreversible changes in pulmonary vasculature.