Open AccessFunctional pulmonary atresia in newborn with normal intracardiac anatomy: Successful treatment with inhaled nitric oxide and pulmonary vasodilators
Author(s) -
Gürkan Altun,
Kadir Babaoğlu,
Köksal Binnetoğlu,
Nazan Kavas,
Ayşe Engin Arısoy
Publication year - 2013
Publication title -
annals of pediatric cardiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.292
H-Index - 19
eISSN - 0974-2069
pISSN - 0974-5149
DOI - 10.4103/0974-2069.107243
Subject(s) - medicine , pulmonary atresia , intracardiac injection , cardiology , pulmonary valve , atresia , tricuspid valve , pulmonary hypertension , nitric oxide , bronchopulmonary dysplasia , pulmonary artery , pregnancy , gestational age , biology , genetics
Functional pulmonary atresia is characterized by a structurally normal pulmonary valve that does not open during right ventricular ejection. It is usually associated with Ebstein's anomaly, Uhl's anomaly, neonatal Marfan syndrome and tricuspid valve dysplasia. However, functional pulmonary atresia is rarely reported in newborn with anatomically normal heart. We report a newborn with functional pulmonary atresia who had normal intracardiac anatomy, who responded to treatment with nitric oxide and other vasodilator therapy successfully.