Open AccessPlacement of an implantable cardioverter-defibrillator in an infant with congenital long QT syndrome: Anesthetic considerations
Author(s) -
Bhuvnesh Kansara,
Ajmer Singh,
Sunil Kaushal,
Anil Saxena
Publication year - 2011
Publication title -
annals of cardiac anaesthesia/annals of cardiac anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.42
H-Index - 27
eISSN - 0974-5181
pISSN - 0971-9784
DOI - 10.4103/0971-9784.81568
Subject(s) - medicine , implantable cardioverter defibrillator , hypertrophic cardiomyopathy , long qt syndrome , sudden cardiac arrest , sudden cardiac death , cardiology , population , brugada syndrome , cardiomyopathy , resuscitation , ventricular fibrillation , qt interval , anesthesia , heart failure , environmental health
Sudden cardiac arrest (SCA) in children is a rare, but catastrophic event. Children with cardiac pathology at particular risk include those with congenital long QT syndrome (CLQTS) and hypertrophic cardiomyopathy. CLQTS is a genetic disorder of the cardiac ion channels and is associated with significant risk of malignant ventricular arrhythmias and SCA. For symptomatic, untreated patients, the mortality rate is approximately 20% for the first year and 50% at ten years. Use of an implantable cardioverter-defibrillator (ICD) is recommended for the prevention of SCA in this patient population. We report a case of CLQTS, who after successful resuscitation from SCA, underwent ICD placement at our center.