Open AccessPrimary pigmented nodular adrenocortical disease
Author(s) -
Marie Therese Manipadam,
Rachel Abraham,
Sudipta Sen,
Anna Simon
Publication year - 2011
Publication title -
journal of indian association of pediatric surgeons
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.306
H-Index - 17
eISSN - 1998-3891
pISSN - 0971-9261
DOI - 10.4103/0971-9261.86881
Subject(s) - carney complex , medicine , adrenalectomy , bilateral adrenalectomy , pathology , disease , dermatology , surgery , biochemistry , chemistry , gene
Primary pigmented nodular adrenocortical disease (PPNAD) is a rare cause of ACTH-independent Cushing's syndrome and has characteristic gross and microscopic pathologic findings. We report a case of PPNAD in a 15-year-old boy, which was not associated with Carney's complex. Bilateral adrenalectomy is the treatment of choice.