Open AccessSynovial sarcoma of kidney in a child: A rare presentation
Author(s) -
Venkatraman Radhakrishnan,
Manikandan Dhanushkodi,
Kathiresan Narayanswamy,
Anand Raja,
Shirley Sundersingh,
Sagar Tenali
Publication year - 2016
Publication title -
journal of indian association of pediatric surgeons
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.306
H-Index - 17
eISSN - 1998-3891
pISSN - 0971-9261
DOI - 10.4103/0971-9261.172502
Subject(s) - medicine , synovial sarcoma , sarcoma , biopsy , wilms' tumor , chemotherapy , presentation (obstetrics) , clear cell sarcoma , regimen , renal biopsy , pathology , radiology , surgery
There are no reported cases in the literature of primary renal synovial sarcoma in pediatric patients. The management of renal synovial sarcoma has been extrapolated from the management of soft tissue sarcomas at other sites. We present a 4-year-old female who was suspected to have Wilms' tumor. The patient underwent guided biopsy as she did not respond to neoadjuvant chemotherapy for Wilms' tumor. The biopsy was consistent with primary renal synovial sarcoma. The child was treated with change in her neoadjuvant chemotherapy regimen and surgery. The diagnosis of synovial sarcoma was confirmed by demonstrating the t (X, 18) translocation using polymerase chain reaction.