Open AccessA rare case of bilateral cystic nephroma associated with embryonal rhabdomyosarcoma of the penile urethra
Author(s) -
Jujju Jacob Kurian,
Sudipta Sen,
Richard Joseph,
Mandeep Singh Bindra
Publication year - 2015
Publication title -
journal of indian association of pediatric surgeons
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.306
H-Index - 17
eISSN - 1998-3891
pISSN - 0971-9261
DOI - 10.4103/0971-9261.151553
Subject(s) - embryonal rhabdomyosarcoma , medicine , rhabdomyosarcoma , urethra , male urethra , urology , pathology , sarcoma
Bilateral cystic nephroma is an extremely rare benign renal neoplasm. Here we present a case of bilateral cystic nephroma in a four month old boy who subsequently developed embryonal rhabdomyosarcoma of the urethra. Both tumors were successfully treated. To our knowledge this is the first reported case of this association which could be related to Dicer-1 mutation.