Open AccessThe Abernethy malformation-myriad imaging manifestations of a single entity
Author(s) -
Samarjit Singh Ghuman,
Saumya Gupta,
T. B. S. Buxi,
Kishan Singh Rawat,
Anurag Yadav,
Naimish Mehta,
Seema Sud
Publication year - 2016
Publication title -
indian journal of radiology and imaging - new series/indian journal of radiology and imaging/indian journal of radiology and imaging
Language(s) - English
Resource type - Journals
eISSN - 0971-3026
pISSN - 0970-2016
DOI - 10.4103/0971-3026.190420
Subject(s) - medicine , portosystemic shunt , radiology , magnetic resonance imaging , portal hypertension , inferior mesenteric vein , computed tomography , transjugular intrahepatic portosystemic shunt , venous malformation , shunt (medical) , superior mesenteric vein , vascular malformation , portal vein , cirrhosis , surgery , gastroenterology
Abernethy malformation, also known as congenital extrahepatic portosystemic shunts (CEPS) is a rare clinical entity and manifests with different clinical symptoms. CEPS are abnormalities of vascular development where there is shunting of portal blood into the systemic venous system. Multidetector computed tomography (MDCT) is a fast and effective modality for evaluation of CEPS. CT displays all the information desired by the surgeon as well as the clinician including the anatomy of the splenic and superior mesenteric veins, size and site of the shunt, presence or absence of the portal vein radicles, and helps to plan the therapy and even the follow-up of these patients. Contrast-enhanced magnetic resonance imaging (MRI) has also emerged as a promising tool for the evaluation of liver lesions associated with the malformation. The Radiologist should be aware of the various imaging appearances of this entity including its complications. In this article, we describe the imaging appearances of CEPS, their complications, and their imaging appearances on CT and MRI. We have also described various associated anomalies.