Open AccessLymphangioleiomyomatosis diagnosed by effusion cytology: A case report
Author(s) -
Glorimar Rivera,
Tunc Gokaslan,
Elizabeth Kurian
Publication year - 2015
Publication title -
journal of cytology/journal of cytology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.267
H-Index - 19
eISSN - 0974-5165
pISSN - 0970-9371
DOI - 10.4103/0970-9371.171256
Subject(s) - medicine , lymphangioleiomyomatosis , tuberous sclerosis , chylothorax , pleural effusion , parenchyma , pathology , effusion , lung , computed tomographic , lymphangiomatosis , cytology , lymphatic system , radiology , computed tomography , surgery
Lymphangioleiomyomatosis (LAM) is a rare lung disease traditionally affecting women during their childbearing years. It can be sporadic or be associated with tuberous sclerosis syndrome. It is usually manifested in the lungs, kidneys, and/or lymphatic system. It consists of an overgrowth of abnormal smooth muscle-like cells, usually along the bronchovascular structures, resulting in the formation of cysts and the destruction of the lung parenchyma. We present the case of a 43-year-old woman with a history of pleural effusion and dyspnea. A computed tomographic scan revealed a mediastinal mass, chylothorax, and multiple pulmonary cysts. A diagnosis of LAM was rendered on a pleural fluid sample.