Open AccessDentinogenesis imperfecta: A review and case report of a family over four generations
Author(s) -
Sudhir Bhandari,
Karneev Pannu
Publication year - 2008
Publication title -
indian journal of dental research/indian journal of dental research
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.277
H-Index - 43
eISSN - 1998-3603
pISSN - 0970-9290
DOI - 10.4103/0970-9290.44543
Subject(s) - dentinogenesis imperfecta , dentinogenesis , permanent dentition , osteogenesis imperfecta , dentin , dentistry , medicine , dentin sialophosphoprotein , dentition , orthodontics , anatomy , odontoblast
Dentinogenesis imperfecta (DGI) is one of the most common hereditary disorders of dentin formation. It follows an autosomal dominant pattern of transmission, affecting both the formation and mineralization of dentin. Either or both primary and permanent dentition is affected by it. This paper briefly reviews the manifestations of DGI Type II (DGI1) and presents a case report of a family affected with DGI1 over four generations.