z-logo
open-access-imgOpen Access
Papillon-Lefevre syndrome: Two case reports
Author(s) -
Jigna S Shah,
S.P. Goel
Publication year - 2007
Publication title -
indian journal of dental research/indian journal of dental research
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 0.277
H-Index - 43
eISSN - 1998-3603
pISSN - 0970-9290
DOI - 10.4103/0970-9290.35834
Subject(s) - medicine , dermatology , deciduous teeth , palmoplantar keratoderma , aggressive periodontitis , permanent teeth , periodontitis , dentistry , pediatrics , hyperkeratosis
Papillon-Lefevre syndrome is a rare autosomal recessive disorder in which there is palmoplantar keratinization and premature loss of both deciduous and permanent teeth. The palmoplantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. An early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. We present two cases of the syndrome having all of the characteristic features.

The content you want is available to Zendy users.

Already have an account? Click here to sign in.
Having issues? You can contact us here