Open AccessDental management of PHACE syndrome under general anesthesia
Author(s) -
S. Fernandes,
Aniket Kakade,
Abdulkadeer M. Jetpurwala,
BS Patil,
Sadhana Jain,
Pankajkumar Ashok Kasar
Publication year - 2011
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/0970-4388.90745
Subject(s) - medicine , bleed , intubation , airway management , airway , hemangioma , anesthesia , surgery
PHACE syndrome was first described by Dr. Ilonia Frieden and colleagues in 1996. It is an under-recognized rather than a very rare condition among patients with large facial hemangiomas. It is challenging as it has significant neurological, vascular and airway implications. Vascular malformations compromising cerebral blood flow predispose the patient to strokes and seizures. Subglottic hemangiomas, if present, could bleed during intubation. Meticulous neurological monitoring is mandatory in those undergoing repair of the great vessels. We describe the perioperative management of a child with PHACE syndrome subjected to dental treatment under general anesthesia.