Open AccessFacial plexiform neurofibroma in a child with neurofibromatosis type I: A case report
Author(s) -
Karthikeya Patil,
VG Mahima,
SK Shetty,
K Lahari
Publication year - 2007
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/0970-4388.31987
Subject(s) - plexiform neurofibroma , pathognomonic , neurofibromatosis , neurofibromatosis type i , neurofibroma , medicine , lesion , pathology , anatomy , disease
Plexiform neurofibroma is a non-circumscribed, thick and irregular benign tumor of the peripheral nerve sheath. It is a virtually pathognomonic and often disabling feature of neurofibromatosis type I. The diffuse and soft nature of plexiform neurofibroma is often compared to 'a bag of worms' and is difficult to distinguish from a vascular malformation or a lymphangioma, thus necessitating thorough clinical and histopathological examination and imaging of the lesion. We present a case of plexiform neurofibroma in a 12-year-old male child.