Open AccessHematological and surgical management in Glanzmann′s thrombasthenia: A case report
Author(s) -
Anjana Gopalakrishnan,
Ravi Veeraraghavan,
Prasanth Panicker
Publication year - 2014
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/0970-4388.131000
Subject(s) - glanzmann's thrombasthenia , thrombasthenia , medicine , enucleation , mucocutaneous zone , platelet disorder , platelet , pediatrics , surgery , platelet membrane glycoprotein , dermatology , platelet aggregation , disease
Glanzmann's thrombasthenia (GT) is a rare, congenital, and moderate to severe platelet disorder. The bleeding time is increased, due to lack of platelet aggregation, since the patients with GT have deficient or dysfunctional integrin membrane glycoproteins IIb and IIIa essential for platelet aggregation. Children with GT are mostly diagnosed very early in life due to the spontaneous and unexplained mucocutaneous bleeding. It is quite a challenging task when any surgery is indicated for children with GT. This case report is about the medical and surgical management of an 11-year-old girl diagnosed with Glannzmann's thrombasthenia who had to undergo a maxillary cyst enucleation.