Open AccessSegmental odontomaxillary dysplasia
Author(s) -
Anand Agrawal,
J. Wozniak Daniel,
Vijeev Vasudevan
Publication year - 2014
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/0970-4388.127071
Subject(s) - medicine , dysplasia , radiography , premolar , soft tissue , anatomy , dentistry , pathology , radiology , molar
Segmental odontomaxillary dysplasia is a type of hemi-maxillofacial dysplasia. It is a sporadic, mesoectodermal dysplasia that presents early in life, possibly as early as in utero and exhibits male gender predominance (1.7:1.0). Its features include enlargement of the soft tissue and/or bone of one hemimaxilla that may produce mild facial asymmetry, sclerotic radiographic bone changes and dental developmental abnormalities. The dense bone, which often exhibits a radiographic vertical orientation of the trabecular bone pattern, is generally associated with delayed eruption of the teeth. Congenitally missing premolar teeth (either or both) is a common feature of this condition that is of significant diagnostic value. Ipsilateral cutaneous findings have been reported in 23% of cases. Immature woven bone forming irregular patterns are seen histologically. Herein, we present a case report on segmental odontomaxillary dysplasia in a 13-year-old boy.