Open AccessFreeman-Sheldon syndrome: A dental perspective
Author(s) -
Bijumon,
Dexton Antony Johns
Publication year - 2013
Publication title -
journal of the indian society of pedodontics and preventive dentistry/journal of indian society of pedodontics and preventive dentistry
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.378
H-Index - 33
eISSN - 1998-3905
pISSN - 0970-4388
DOI - 10.4103/0970-4388.117978
Subject(s) - microstomia , medicine , camptodactyly , dental hygiene , ulnar deviation , dentistry , orthodontics , pediatrics , physical therapy , surgery , range of motion
Freeman-Sheldon syndrome is a rare progressive myopathic disorder affecting the face, chest, and limbs. It is characterized by three basic abnormalities: microstomia with pouting lips, camptodactyly with ulnar deviation of the fingers, and talipes equinovarus. Presence of microstomia is always associated with practical difficulties of oral hygiene maintenance and increased susceptibility to caries. Patient as well as parental counseling is important in these cases. This case report presents a 7-year-old child with Freeman-Sheldon syndrome. Emphasis is given for the dental management of such children.