Open AccessDiagnostic role of magnetic resonance angiography in Swyer James syndrome: Case series of two cases
Author(s) -
Umesh C Parashari,
Ragini Singh,
Anit Parihar,
Pallavi Aga,
Rajesh Yadav
Publication year - 2010
Publication title -
lung india
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.457
H-Index - 25
eISSN - 0974-598X
pISSN - 0970-2113
DOI - 10.4103/0970-2113.68326
Subject(s) - medicine , vascularity , air trapping , radiology , bronchiectasis , magnetic resonance angiography , chest radiograph , magnetic resonance imaging , angiography , lung , radiography , computed tomography
Swyer James syndrome is a rare syndrome which occurs due to viral illness in early childhood. The post infective obliterative bronchiolitis results in arrest of lung growth and alveolarization with reduced vascularity resulting in classical radiological features. We describe two cases of patients fulfilling all the criteria of the syndrome - 1) Unilateral hyperlucent small lung in chest radiograph with air trapping on expiration, small ipsilateral hila and pulmonary artery. 2) Diffuse decrease in attenuation of lung parenchyma with bronchiectasis and reduction in vascularity. 3) Unilateral pruned tree appearance on angiography (MRA). The clinical presentation was recurrent chest infection in a child and infrequent bouts of hemoptysis in a middle aged female. The study demonstrates the role of magnetic resonance angiography in diagnosing the condition.