Open AccessMammoth orbitofrontal neurofibromatosis with herniating meningo-encephalocele
Author(s) -
Prema Dhanraj,
Kingsly Paul,
Shashank Lamba,
Rahul Shetty
Publication year - 2010
Publication title -
indian journal of plastic surgery/indian journal of plastic surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.299
H-Index - 29
eISSN - 1998-376X
pISSN - 0970-0358
DOI - 10.4103/0970-0358.63957
Subject(s) - encephalocele , medicine , neurofibromatosis , mammoth , neurofibroma , orbit (dynamics) , surgery , foregut , anatomy , radiology , paleontology , biology , engineering , aerospace engineering
We are presenting a mammoth orbito-frontal neurofibroma with a herniating meningo-encephalocele in a 23 year old African male. The tumour measured 87cm x 54cm and occupied the right orbito-temporo-facial region and had destroyed the right orbit. A pre operative embolization of the feeding vessels was followed by a one stage near total excision of the tumour and repair of the meningo-encephalocele in hypotensive anaesthesia. The excised tumour weighed 8 Kg and, to the best of our knowledge, is the largest orbito-facial neurofibroma reported in literature.