Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease | Zendy

Kim Vaiphei | Zendy; K. P. Srikanth | Zendy; Inusha Panigrahi | Zendy; BabuRam Thapa | Zendy

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Severe liver dysfunction in an infant with cystic fibrosis masquerading as metabolic liver disease

Author(s) -

Kim Vaiphei,

K. P. Srikanth,

Inusha Panigrahi,

BabuRam Thapa

Publication year - 2016

Publication title -

indian journal of pathology and microbiology

Language(s) - English

Resource type - Journals

SCImago Journal Rank - 0.217

H-Index - 31

eISSN - 0974-5130

pISSN - 0377-4929

DOI - 10.4103/0377-4929.188137

Subject(s) - cystic fibrosis , medicine , pathology , cholestasis , polycystic disease , congenital hepatic fibrosis , pancreas , disease , gastroenterology , liver disease , lung , portal hypertension , kidney , cirrhosis

We present a rare presentation of cystic fibrosis with neonatal cholestasis. Histological features of mucoviscidosis were present in liver involving the biliary tract, intestinal mucosa, pancreas, and lung. Besides, there was a rare association with autosomal dominant type of polycystic renal disease.

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