Open AccessRecurrent multifocal cutaneous Kaposiform hemangioendothelioma: A rare vascular tumor of infancy and childhood
Author(s) -
Bhagyalakshmi Atla,
Pushpalatha Sudhakar,
Nagarjun Rao,
Prasad Uma
Publication year - 2016
Publication title -
indian journal of pathology and microbiology/indian journal of pathology and microbiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.217
H-Index - 31
eISSN - 0974-5130
pISSN - 0377-4929
DOI - 10.4103/0377-4929.188130
Subject(s) - medicine , kasabach–merritt syndrome , chin , nose , hemangioendothelioma , sarcoma , vascular tumor , hemangioma , soft tissue , capillary hemangioma , pathology , dermatology , surgery , anatomy
Kaposiform hemangioendothelioma (KHE) is a locally aggressive vascular tumor of childhood although cases occurring in adulthood are also described. The features overlap with juvenile capillary hemangioma and Kaposi sarcoma. We report a rare case of recurrent, multifocal (nose and chin) cutaneous KHE initially occurring in a 3-year-old female child, uncomplicated by Kasabach-Merritt syndrome. Recurrences occurred over the next 6 years and resulted in complete distortion of the nose, requiring plastic repair.