Open AccessLower limbs deformities in patients with McCune-Albright syndrome: Tomography and treatment
Author(s) -
Ali Al Kaissi,
Vladimir Kenis,
Farid Ben Chehida,
Jochen G. Hofstaetter,
Franz Grill,
G. Rudolf
Publication year - 2016
Publication title -
african journal of paediatric surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.163
H-Index - 17
eISSN - 0189-6725
pISSN - 0974-5998
DOI - 10.4103/0189-6725.187808
Subject(s) - medicine , mccune–albright syndrome , deformity , intramedullary rod , polyostotic fibrous dysplasia , surgery , fibrous dysplasia , precocious puberty , hormone
The skeletal changes in McCune-Albright disease are usually severe because of the polyostotic form of the disease. Trendelenberg gait and limited mobility are the most common presenting features. The constellation of Café-au lait spots and polyostotic bone involvement is commonly referred to as McCune-Albright's syndrome (MAS).