Open AccessManagement of digestive lesions associated to congenital epidermolysis bullosa
Author(s) -
J. Chahed,
Mongi Mekki,
Amine Ksia,
Nehla Kechiche,
Saida Hidouri,
Trimech Monia Youssef,
Lassâad Sahnoun,
I. Krichéne,
Mohsen Belghith,
Abdellatif Nouri
Publication year - 2015
Publication title -
african journal of paediatric surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.163
H-Index - 17
eISSN - 0189-6725
pISSN - 0974-5998
DOI - 10.4103/0189-6725.172544
Subject(s) - medicine , epidermolysis bullosa , pyloroplasty , scars , surgery , genodermatosis , retrospective cohort study , atresia , dermatology , pediatrics , biochemistry , chemistry , duodenal ulcer , gene
Congenital epidermolysis bullosa (CEB) is a rare genodermatosis. The digestive system is very frequently associated with skin manifestations. Pyloric atresia (PA) and oesophageal stenosis (OS) are considered the most serious digestive lesions to occur.The aim of this work is to study the management and the outcome of digestive lesions associated to CEB in four children and to compare our results to the literature.