Open AccessEarly abdomino-perineal pull-through vaginoplasty
Author(s) -
İlhan Çiftçi,
Ayhan Taştekın,
Alı Annagür,
Mustafa Koplay
Publication year - 2013
Publication title -
african journal of paediatric surgery
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.163
H-Index - 17
eISSN - 0189-6725
pISSN - 0974-5998
DOI - 10.4103/0189-6725.115053
Subject(s) - vaginoplasty , medicine , renal agenesis , mullerian ducts , respiratory distress , müllerian mimicry , gynecology , uterus , surgery , vagina , endocrinology , kidney , pathology
Vaginal agenesis is known as one of the Müllerian anomalies. Müllerian anomalies occur during gonadal development and differentiation, and may lead to complex outcomes. McKusick-Kaufman syndrome (MKS) is an autosomal recessive multiple malformation syndrome characterized by Müllerian anomalies with hydrometrocolpos (HMC) and postaxial polydactyly (PAP). We report a case of a female newborn that developed hydronephrosis and respiratory distress due to compression of the cystic mass and underwent surgery on postpartum day 3. Pull-through vaginoplasty was performed with an abdomino-perineal approach. We report the unique treatment approach in this case.