Open AccessTransformation of dermatofibrosarcoma protuberans into a fibrosarcoma
Author(s) -
Mohamed Ali Sbai,
Sofien Benzarti,
Khaled Bouzaïdi,
Feten Sbei,
Riadh Mhiri
Publication year - 2016
Publication title -
indian journal of dermatology/indian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.395
H-Index - 36
eISSN - 1998-3611
pISSN - 0019-5154
DOI - 10.4103/0019-5154.174129
Subject(s) - dermatofibrosarcoma protuberans , medicine , fibrosarcoma , malignancy , malignant transformation , dermatofibrosarcoma , metastasis , dermatology , transformation (genetics) , pathology , cancer , biology , biochemistry , gene
Dermatofibrosarcoma protuberans is a rare cutaneous mesenchymal tumor characterized by a low potential of malignancy with a very low rate of metastasis but an important rate of local recurrence. Its transformation into a fibrosarcoma is exceptional, responsible for a higher metastatic potential. This transformation implies a closer surveillance. Through a case report and literature review, we will try to expose epidemiological, clinical, histological, therapeutic, and outcome particularities of this entity