Open AccessUnilateral, linear blue rubber bleb nevus syndrome (Bean′s syndrome): An unfamiliar presentation: First case from India
Author(s) -
Karan Sancheti,
Indrashis Podder,
Anupam Das,
Sourav Choudhury,
Somodyuti Chandra,
Ramesh Chandra Gharami
Publication year - 2015
Publication title -
indian journal of dermatology/indian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.395
H-Index - 36
eISSN - 1998-3611
pISSN - 0019-5154
DOI - 10.4103/0019-5154.159644
Subject(s) - medicine , hematochezia , nevus , presentation (obstetrics) , blue nevus , surgery , dermatology , colonoscopy , colorectal cancer , melanoma , cancer research , cancer
Blue rubber bleb nevus syndrome (BRBNS) also called Bean's syndrome is a rare disorder characterized by multiple cutaneous venous malformations in association with visceral lesions, most commonly affecting the gastrointestinal tract. We report here, a 21-year-old woman patient, who presented with unilateral, blaschkoid distribution of cutaneous venous malformations along with blue rubber bleb nevus and recurrent episodes of hematochezia due to vascular lesions in the sigmoid colon; likely to be a case of BRBNS. The unusual unilateral, blaschkoid distribution of BRBNS prompted this present report.