Open AccessAdult-onset unilateral disabling pansclerotic morphea
Author(s) -
Adarshlata Singh,
Kritika Singhal,
Sanjiv Choudhary,
Shazia Bisati,
Mallika Arora
Publication year - 2014
Publication title -
indian journal of dermatology/indian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.395
H-Index - 36
eISSN - 1998-3611
pISSN - 0019-5154
DOI - 10.4103/0019-5154.131459
Subject(s) - medicine , morphea , elbow , contracture , presentation (obstetrics) , surgery , subcutaneous tissue , joint contracture , dermatology , dermis , anatomy , lichen sclerosus
Disabling pansclerotic morphea (DPM) is a rare, severe, and mutilating form of morphea, involving the dermis, subcutaneous tissue, fat, muscle, and even bone. It is usually seen before the age of 14 years, with the patient complaining of arthralgia and stiffness at the time of onset. We report a case of unilateral adult-onset DPM with sparing of the face. Within a few months of onset, painful contracture deformities of the hand, elbow, and shoulder joints developed, impairing the patient′s normal daily activities. We are reporting this case because of the unusual presentation: DPM in an adult, with history of trauma in childhood and rapid onset of complications, is rare