Open AccessA case of adult-onset Still′s disease presenting with urticated plaques and acute myopericarditis
Author(s) -
Noor Hanif Said,
Siew Ngoh Wong,
Wei Hsia Tan
Publication year - 2013
Publication title -
indian journal of dermatology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.395
H-Index - 36
eISSN - 1998-3611
pISSN - 0019-5154
DOI - 10.4103/0019-5154.117316
Subject(s) - myopericarditis , medicine , rash , adult onset still's disease , dermatology , etiology , differential diagnosis , disease , azathioprine , malignancy , arthritis , pericarditis , pathology , immunology
Adult onset Still′s disease (AOSD) is a systemic inflammatory disorder of unknown etiology characterized by spiking fever, evanescent skin rash, arthralgia or arthritis, involvement of various organs, and predominantly neutrophilic leucocytosis. AOSD, although uncommon, has a characteristic constellation of clinical and laboratory features and should be considered in the differential diagnosis of pyrexia of unknown origin associated with a rash and arthralgia. The diagnosis is one of clinical suspicion and it is essential that infections, malignancy, and other rheumatic diseases are excluded. We report a case which illustrates the typical features of AOSD that were treated with steroids and azathioprine