Open AccessAnaesthetic consideration in patients with Gorham′s syndrome: A case report and review of the literature
Author(s) -
Rajendra Kumar Sahoo,
Jagannathan Balavenkatasubramanian,
Palanichamy Gurumoorthi,
N Vivekanand
Publication year - 2012
Publication title -
indian journal of anaesthesia/indian journal of anaesthesia
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.645
H-Index - 30
eISSN - 0976-2817
pISSN - 0019-5049
DOI - 10.4103/0019-5049.100831
Subject(s) - medicine , general anaesthesia , prone position , surgery , airway management , airway , decompression , airway obstruction , intensive care medicine , anesthesia
Gorham's syndrome (GS) is a rare disorder characterized by proliferation of vascular channels resulting in destruction and resorption of osseous matrix leading to bone loss. Bone loss leads to joint instability and problems during airway management and positioning for surgery. Respiratory involvement further complicates anaesthesia management. We report the anaesthetic care of a 21-year-old male patient of known GS for spine decompression and fusion in prone position. Airway management, induction technique, pathophysiology of the disease, drug selection and other concerns of anaesthesia for major spine surgery has been discussed reviewing the sparse literature available.