Open AccessDyke–Davidoff–Masson syndrome with crossed cerebellar atrophy
Author(s) -
Sanjay M. Khaladkar,
Shishir Chauhan,
Amit Patil,
Siddappa Gurubalappa Gandage,
Surbhi Chauhan Kalra
Publication year - 2017
Publication title -
sa journal of radiology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.18
H-Index - 3
eISSN - 2078-6778
pISSN - 1027-202X
DOI - 10.4102/sajr.v21i1.1207
Subject(s) - medicine , atrophy , hemiparesis , anatomy , cerebellar hemisphere , cerebellum , pathology , lesion
Dyke–Davidoff–Masson syndrome is a rare condition with classical, clinical and radiological changes – mental retardation, hemiparesis, facial asymmetry, seizures and cerebral hemiatrophy with calvarial changes. Contralateral cerebellar atrophy is rare and occurs if insult occurs after 1 month of age. We report a case of a 6-year-old female child presenting with right-sided hemiparesis, convulsions and left cerebral hemiatrophy with an old infarct in left middle cerebral artery (MCA) territory, ipsilateral calvarial thickening and right (crossed) cerebellar atrophy.