Open AccessKistifibrose
Author(s) -
D.E. Pera
Publication year - 1981
Publication title -
curationis
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.408
H-Index - 21
eISSN - 2223-6279
pISSN - 0379-8577
DOI - 10.4102/curationis.v4i1.510
Subject(s) - cystic fibrosis , pancreatic enzymes , mucus , sweat , medicine , disease , pancreatic disease , lung , gastroenterology , pancreas , physiology , intensive care medicine , biology , ecology
Cystic fibrosis is a recessively inherited inborn error of metabolism which causes abnormal functioning of mucus and sweat glands. The disease manifests itself with varying degrees of chronic lung disease, pancreatic enzyme deficiency as well as loss of salt and water in the sweat, all of which may lead to secondary complications. Treatment is aimed mainly at the removal of mucus from bronchial passages and the dietary correction of the pancreatic enzyme deficiency. As this is a chronic disease the education and support of the patient and his family are important aspects of nursing care