Open AccessThe importance of patient reported functional outcome in paediatric desmoid fibromatosis
Author(s) -
Gurhan Erturan,
Harriet Holme,
Anna Cassoni,
Roberto Tirabosco,
Rob Pollock,
Tim Briggs,
Maria Michelagnoli
Publication year - 2012
Publication title -
rare tumors
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.285
H-Index - 15
eISSN - 2036-3613
pISSN - 2036-3605
DOI - 10.4081/rt.2012.4418
Subject(s) - medicine , fibromatosis , dermatology , pathology
Desmoid fibromatosis (DF) is a heterogeneous condition with lack of consensus regarding therapy. Fatality is rare but repeated surgery prevalent. Functional assessment for this group is not well established, although we believe it to be an important marker of treatment success. At present there is no validated objective or subjective functional assessment tool designed for benign but locally invasive disease