Open AccessThe portopulmonary hypertension: an overview from diagnosis to treatment
Author(s) -
Andrea Salzano,
Domenico Sirico,
Luisa Golia,
Valentina Faga,
Martina Flora,
Eduardo Bossone,
Antonio Cittadini
Publication year - 2015
Publication title -
monaldi archives for chest disease. pulmonary series/monaldi archives for chest disease/monaldi archives for chest disease. cardiac series
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.196
H-Index - 46
eISSN - 2465-101X
pISSN - 1122-0643
DOI - 10.4081/monaldi.2013.81
Subject(s) - portopulmonary hypertension , portal hypertension , medicine , computer science , intensive care medicine , cirrhosis
Portopulmonary hypertension (POPH) refers to the condition of pulmonary arterial hypertension (PAH) in association with portal hypertension. Among patients with portal hypertension, reported incidence rates of POPH range from 2 to 10% and long-term prognosis in cases of POPH is poor. Fundamental issues of management of POPH include identification of patients likely to benefit from liver transplantation (LTx) and treatment with specific pulmonary vasodilators before and after LTx. This review presents as an overview of the current knowledge on the epidemiology, diagnosis, treatment and prognosis of patients with portopulmonary hypertension.