Open AccessErdheim-Chester disease with rare radiological features in a 14-year old girl with pre-B Acute Lymphocytic Leukemia and Diabetes mellitus
Author(s) -
Varanasi Venkata Rama Krishna,
Teo Eu Leong Harvey James,
Kenneth Tou En Chang,
Soh Shui Yen
Publication year - 2014
Publication title -
journal of radiology case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.154
H-Index - 18
ISSN - 1943-0922
DOI - 10.3941/jrcr.v8i8.1899
Subject(s) - medicine , erdheim–chester disease , girl , histiocytosis , radiological weapon , diabetes mellitus , disease , rare disease , langerhans cell histiocytosis , dermatology , pediatrics , pathology , radiology , endocrinology , psychology , developmental psychology
We report a case of a 14 year-old girl with Diabetes Mellitus who was in remission with pre-B cell Acute Lymphoblastic Leukemia and subsequently diagnosed with Erdheim-Chester disease. Erdheim-Chester disease is a non-Langerhans cell histiocytosis and is very rare in children. In addition, the radiological features of the lesions are atypical and have not been reported in children. There is no known association between the three conditions and this is the first reported case in the literature. A literature review of Erdheim-Chester disease will be performed.