Open AccessAdolescent Type 2 Autoimmune Pancreatitis
Author(s) -
김소현,
백승호,
김혜영,
최수진,
김지훈,
이세희,
김명환
Publication year - 2020
Publication title -
the korean journal of medicine
Language(s) - English
Resource type - Journals
eISSN - 2289-0769
pISSN - 1738-9364
DOI - 10.3904/kjm.2020.95.2.114
Subject(s) - autoimmune pancreatitis , medicine , pancreatitis , pancreas , acute pancreatitis , autoimmune disease , pancreatic disease , biopsy , igg4 related disease , autoimmunity , disease , pathology , gastroenterology
There are two forms of autoimmune pancreatitis (AIP). Type 1 is associated with immunoglobulin G4 (IgG4)-related systemic fibro- inflammatory disease, whereas type 2 AIP is localized to the pancreas and not associated with IgG4. The number of children presenting with type 2 AIP has recently increased. Here, we report a case of type 2 AIP in a 16-year-old adolescent who presented with clinical acute pancreatitis and associated pancreatic masses. He was diagnosed with type 2 AIP based on pancreatic biopsy results showing granulocytic epithelial lesions and supportive radiological imaging and steroid responsiveness.