Open AccessHerlyn Werner Wunderlich Syndrome with Hematocolpos Symptom
Author(s) -
Muhammad Rusda,
Amru Umara,
Andrina Yunita Murni Rambe
Publication year - 2019
Publication title -
open access macedonian journal of medical sciences
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.288
H-Index - 17
ISSN - 1857-9655
DOI - 10.3889/oamjms.2019.406
Subject(s) - medicine , uterus didelphys , renal agenesis , mesonephric duct , menstruation , menarche , physical examination , agenesis , abdominal pain , palpation , gynecology , radiology , surgery , uterus , kidney
BACKGROUND: Uterodidelphys with obstructed hemivagina and ipsilateral renal agenesis is referred to as the Herlyn Werner Wunderlich (HWW) syndrome. Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract involving Müllerian ducts and Wolffian structures, and it is Werner by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis.
CASE REPORT: Here, we describe a 17-year-old female patient presented with severe and increasing cyclical abdominal pain. She attained menarche 3 years back. The patient had irregular and scanty menstruation associated with dysmenorrhoea. On physical examination, secondary sexual characters were well developed, and on palpation, lower abdomen tenderness was not present. Diagnosed with HWW syndrome, who was taken up for diagnostic sonography and MRI, followed by vaginal septal resection,
CONCLUSION: In addition to a definitive diagnosis, this approach helped in symptomatic relief to the patient.