Open AccessAn unusual presentation of primary sclerosing cholangitis
Author(s) -
Franklin Goldwire,
William E. Norris,
Jonathan M. Koff,
Zachary Goodman,
Milton T. Smith
Publication year - 2008
Publication title -
world journal of gastroenterology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.427
H-Index - 155
eISSN - 2219-2840
pISSN - 1007-9327
DOI - 10.3748/wjg.14.6748
Subject(s) - medicine , endoscopic retrograde cholangiopancreatography , primary sclerosing cholangitis , choledochal cysts , liver biopsy , biliary cirrhosis , biopsy , gastroenterology , presentation (obstetrics) , cirrhosis , radiology , cyst , pancreatitis , disease , autoimmune disease
This case report describes the unusual presentation of a patient who had findings which were initially suggestive of a type IV choledochal cyst. Her liver biopsy demonstrated biliary cirrhosis. She was treated with endoscopic retrograde cholangiopancreatography and biliary stent exchanges over one year. Her cholangiogram one year later demonstrated resolution of the biliary cystic dilation which led to her initial diagnosis, with beading and stricturing of the hepatic ducts consistent with primary sclerosing cholangitis. Liver-associated enzymes and physical findings also improved. A liver biopsy one year later demonstrated a marked improvement in hepatic fibrosis with no evidence of cirrhosis.