Open AccessRecurrent Cervical Neurofibrosarcoma: A Rare Case of Malignant Peripheral Nerve Sheath Tumor of Head and Neck Region
Author(s) -
Mubashir Malik,
Zubair Khan,
Umer Farooq,
Shehzad Safdar,
Asad Ur Rehman,
Noman Saleem
Publication year - 2022
Publication title -
pakistan journal of neurological surgery
Language(s) - English
Resource type - Journals
eISSN - 2409-5567
pISSN - 1995-8811
DOI - 10.36552/pjns.v25i4.603
Subject(s) - medicine , neurofibromatosis , malignant peripheral nerve sheath tumor , head and neck , radiation therapy , nerve sheath neoplasm , chemotherapy , surgery , radiology
Neurofibrosarcoma is a malignant peripheral nerve sheath tumor (MPNST). The cervical location of the neurofibrosarcoma is very rare and is less than 1% in the literature. MPNSTs are often associated with neurofibromatosis type 1 (NF1). We are presenting a case report of 31 years old female, with huge recurrent cervical neurofibrosarcoma on the right side of the neck. To date, surgical excision followed by chemotherapy and radiotherapy is the treatment of choice which requires a multidisciplinary approach. We excised the above-mentioned cervical neurofibrosarcoma in a piecemeal fashion and discharged the patient on follow-up with the oncology department.