Open AccessDilated Cardiomyopathy Revealing a Henoch-Schönlein Purpura in a Young Patient: About a Case and Review of the Literature…
Author(s) -
Laila Chemaou El Fihri,
Ikram Hazzazi,
Mohammed Eljamili,
Mustapha El Hattaoui
Publication year - 2022
Publication title -
scholars journal of medical case reports
Language(s) - English
Resource type - Journals
eISSN - 2347-9507
pISSN - 2347-6559
DOI - 10.36347/sjmcr.2022.v10i02.008
Subject(s) - medicine , rituximab , purpura (gastropod) , etiology , dilated cardiomyopathy , vasculitis , thrombocytopenic purpura , cardiomyopathy , restrictive cardiomyopathy , dermatology , pathology , immune system , heart failure , immunology , antibody , disease , ecology , biology
Schönlein-Henoch purpura is a non-thrombocytopenic systemic vasculitis of small-caliber vessels due to immune complexes. We report the case of an adult 30 year old man admitted for a generalized edematous syndrome with purpuric lesions in the 2 lower limbs revealing a dilated cardiomyopathy whose etiological assessment was in favor of a Schönlein-Henoch purpura with cardiac, renal, dermatological involvement. The diagnosis was difficult to establish given the clinical polymorphism. Also, management was complicated given the multifocal involvement. The treatment was based on corticosteroid therapy and rituximab but the evolution was, unfortunately, not satisfactory.