Open AccessMedullary Lesions in Erdheim Chester Disease: A Case Report
Author(s) -
Zakaria Chandide Tlemcani,
Imadeddine Sahri,
Abderrahmane Housni,
Jawad Laaguili,
Abad Cherif El Asri,
Miloudi Gazzaz
Publication year - 2022
Publication title -
scholars journal of applied medical sciences
Language(s) - English
Resource type - Journals
eISSN - 2347-954X
pISSN - 2320-6691
DOI - 10.36347/sjams.2022.v10i02.002
Subject(s) - erdheim–chester disease , medicine , diabetes insipidus , histiocytosis , pathology , spinal cord , osteosclerosis , central nervous system , medullary cavity , disease , psychiatry
ERDHEIM CHESTER disease (ECD) called also non-Langerhans Histiocytosis, is a rare illness, which can present various unusual clinical aspects. It is a Histiocytosis characterized by an infiltration of various tissues and organs, bones, retroperitoneum, pleuro-pulmonary sites, skin, and central nervous system. The most frequent central nervous system manifestations of ECD are diabetes insipidus, cerebellar syndromes, orbital lesions, and extra-axial masses involving the dura and here we report a rare case with spinal cord compression on the context of ERDHEIM CHESTER disease. Our work highlights another different clinical, radiological and pathological manifestation associated with ECD that should be considered.