Open AccessKartagener's Syndrome a Case Report and Literature Review
Author(s) -
Diarra Daouda,
Boussa Tressia Carole,
Salihou Abdoulfatihi,
Tabakh Houria,
Siwane Abdellatif,
Touil Najwa,
Kacimi Omar,
N. Çhikhaoui
Publication year - 2022
Publication title -
sas journal of medicine
Language(s) - English
Resource type - Journals
ISSN - 2454-5112
DOI - 10.36347/sasjm.2022.v08i02.011
Subject(s) - primary ciliary dyskinesia , kartagener syndrome , situs inversus , bronchiectasis , medicine , pediatrics , chronic sinusitis , genetic disorder , emergency department , sinusitis , dermatology , surgery , disease , lung , psychiatry
Kartagener syndrome is a very rare genetic disorder with autosomal recessive inheritance, characterized by a triad of chronic bronchorrhea with bronchiectasis, chronic sinusitis and situs inversus. It is part of a syndrome of primary ciliary immobility called primary ciliary dyskinesia. Imaging is the key examination in the workup of Kartagener's syndrome and is usually discovered during a CT scan. The treatment is essentially symptomatic and preventive based on the treatment of episodes of respiratory superinfections, physiotherapy for bronchial drainage and anti-influenza and anti-pneumococcal vaccinations. We report a case of Kartagener's syndrome collected in the radiology department of the emergency room.